Multiple pilomatricomas: A Rare Case Report

Reza Azadi, Kambiz Kamyab Hesari, Touba Abbasi

Abstract


A pilomatricoma is an uncommon tumor originating from hair matrix cells. This tumor most commonly presents on the head and neck region. Multiple pilomatricomas is a rare variant of pilomatricoma may be sporadic, familial, or syndromic (Gardner syndrome, myotonic dystrophy and Turner syndrome) that usually presents as an asymptomatic, rapidly growing, keloid-like lesion in the upper arms or shoulders. We report an unusual case of pilomatricoma on the left arm and left flank of nine-year-old boy. The lesions are smooth-surfaced and firm consistency. The histologic examination shows irregular nests of basaloid cells with different stages of trichocyte differentiation and the formation of ghost cells in the dermis

A pilomatricoma is an uncommon tumor originating from hair matrix cells. This tumor most commonly presents on the head and neck region. Multiple pilomatricomas is a rare variant of pilomatricoma may be sporadic, familial, or syndromic (Gardner syndrome, myotonic dystrophy and Turner syndrome) that usually presents as an asymptomatic, rapidly growing, keloid-like lesion in the upper arms or shoulders. We report an unusual case of pilomatricoma on the left arm and left flank of nine-year-old boy. The lesions are smooth-surfaced and firm consistency. The histologic examination shows irregular nests of basaloid cells with different stages of trichocyte differentiation and the formation of ghost cells in the dermis.


Keywords


Multiple pilomatricomas, anetoderma pilomatricomas, skin tumor

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References


Forbis, R., Jr. and E.B. Helwig, Pilomatrixoma (calcifying epithelioma). Arch Dermatol, 1961. 83: p. 606-18.

Jones, C.D., et al., Pilomatrixoma: A Comprehensive Review of the Literature. Am J Dermatopathol, 2018. 40(9): p. 631-641.

Vazquez-Osorio, I., et al., Anetodermic pilomatricoma: clinical, histopathologic, and sonographic findings. Dermatol Online J, 2017. 23(3).

Yagi, Y., et al., Coexistence of keloids and pilomatricoma in a patient with Rubinstein-Taybi syndrome. Dermatol Online J, 2018. 24(1).


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